由于本症预后较差，且各分型又常与其他先心病合并出现，行多普勒超声心动图易漏诊；基层医院无条件进行心血管造影、CT等检查。一旦发现：（1）被诊为动脉导管未闭，并早期出现发绀及肺动脉高压和右向左分流者；（2）X线胸片示主动脉增宽，双肺纹理不对称为其特征，右下动脉干其始较高或有肺动脉观察不清，被怀疑为右肺动脉缺如或发育不良者；（3）右心房、右心室或双侧心室增大者；（4）超声心动图示主动脉直接延续为单侧肺动脉，而另一侧肺动脉不能探及者；应高度警惕本症的存在，以使患者及时得到诊治，减少死亡率。
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